peripheral primitive neuroectodermal tumor of the pelvis
نویسندگان
چکیده
the primitive neuroectodermal tumor (pnet) belongs to a group of highly malignant tumors and is composed of small round cells of a neuroectodermal origin. categorized in the same tumor family as ewing sarcoma, the pnet is most likely to occur in bones and soft tissues. however, a small number of pnet cases arising in the pelvis have been reported as well. we present three cases of pelvic pnet: two cases in the ovary and one case in the broad ligament. the pnet often exhibits aggressive clinical behavior with worse outcomes than other small round cell tumors. the significant prognostic factors of the pnet include site of tumor, volume of neoplasm, and presence of metastasis. the treatment protocol is multimodal and includes local surgical treatment followed by chemotherapy. we herein describe three pnet cases as a rare entity in the pelvis. pelvic pnets should be included in the differential diagnosis of pelvic masses.
منابع مشابه
Peripheral Primitive Neuroectodermal Tumor of the Pelvis
The primitive neuroectodermal tumor (PNET) belongs to a group of highly malignant tumors and is composed of small round cells of a neuroectodermal origin. Categorized in the same tumor family as Ewing sarcoma, the PNET is most likely to occur in bones and soft tissues. However, a small number of PNET cases arising in the pelvis have been reported as well. We present three cases of pelvic PNET: ...
متن کاملPeripheral Primitive Neuroectodermal Tumor of the Pelvis
UNLABELLED The primitive neuroectodermal tumor (PNET) belongs to a group of highly malignant tumors and is composed of small round cells of a neuroectodermal origin. Categorized in the same tumor family as Ewing sarcoma, the PNET is most likely to occur in bones and soft tissues. However, a small number of PNET cases arising in the pelvis have been reported as well. WE PRESENT THREE CASES OF ...
متن کاملPrimitive Neuroectodermal Tumor of the Kidney
Primitive neuroectodermal tumor (PENETs) is an uncommon malignancy of bone and soft tissue witch rarely occurs in the kidney. In more than 90% of the cases, the tumor cells relieves a balanced translocation (11; 22) (q24; q12). Immunohistochemical staining may be required for diagnosis of PENET. The cells of tumor express CD99, vimentin, NSE, FL1 but do not express Ck, LCA, myogenin, and WT1. W...
متن کاملPeripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases
Peripheral primitive neuroectodermal tumor (pPNET) is a highly aggressive small round cell tumor belonging to PNET/Ewing sarcoma family. Ovarian tumors composed of primitive neuroectodermal elements are extremely rare. Herein we reported two cases of peripheral primitive neuroectodermal tumors of ovary in two patients with different clinical presentations. Definite diagnoses were made bas...
متن کاملCongenital Primitive Neuroectodermal Tumor (PNET) of the Orbit
Purpose: To report a case of the congenital primitive neuroectodermal tumor (PNET) of the orbit. Case Report: The patient was a 2-week-old neonate referred to the oculoplastic clinic with right eye proptosis from birth. The neonate was a full term with a history of difficult vaginal delivery. At an initial examination, the ecchymosis of the medial right upper lid was noted. At an initial CT sca...
متن کاملprimitive neuroectodermal tumor of the kidney
primitive neuroectodermal tumor (penets) is an uncommon malignancy of bone and soft tissue witch rarely occurs in the kidney. in more than 90% of the cases, the tumor cells relieves a balanced translocation (11; 22) (q24; q12). immunohistochemical staining may be required for diagnosis of penet. the cells of tumor express cd99, vimentin, nse, fl1 but do not express ck, lca, myogenin, and wt1. w...
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عنوان ژورنال:
iranian journal of medical sciencesجلد ۳۹، شماره ۱، صفحات ۷۱-۰
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